ea0035p546 | Endocrine tumours and neoplasia | ECE2014
Monteiro Ana Margarida
, Alves Marta
, Souto Selma
, Manso Fernando
, Cruz Mariana
, Marques Olinda
Introduction: The pheochromocytomas are rare neuroendocrine tumors that can occur sporadically or, in about 30% of cases, in the context of family syndromes. Ten percent are malignant. Neurofibromatosis type 1 is an autosomal dominant disease that is associated with the occurrence of these tumors. Pheochromocytoma appears at 0.1 5.7% of patients with neurofibromatosis type 1, and are usually solitary and benign lesions.Clinical case: A 50-year-old ...